A rare case of a 5- year- old girl with Klippel–Trénaunay syndrome and a bleeding focal vulvar hemangioma in Uganda

Abstract

Klippel–Trénaunay syndrome (KTS) is a rare congenital disorder marked by bone and soft tissue hypertrophy, port- wine stains, and varicosities. Cases in volving genital hemangiomas are rare. This report highlights a 5- year- old girl in Uganda with typical KTS features, including hypertrophy and port- wine stains, along with a bleeding vulvar hemangioma, emphasizing its uncommon presen tation and potential complications. Treatment involved compression bandaging and timolol 0.2% solution. This case underscores the importance of awareness of atypical manifestations of hemangiomas with KTS and continuous follow- up for female patients, especially through adolescence and pregnancy, due to potential complications such as prepubertal per vaginal bleeding, menorrhagia, and post- partum bleeding.